Gene UniProt Gene Full Name Protein Class N. diseases g DSI g DPI g pLI Score gda EL gda EI gda N. PMIDs N. SNPs gda First Ref. Last Ref.
Entrez Id: 4549
Gene Symbol: RNR1
RNR1
A0A0C5B5G6 s-rRNA 75 0.626 0.769 0.300 None 1.000 4 0 1997 2005
Entrez Id: 286002
Gene Symbol: SLC26A4-AS1
SLC26A4-AS1
SLC26A4 antisense RNA 1 7 0.861 0.269 0.100 None 0 2
Entrez Id: 7399
Gene Symbol: USH2A
USH2A
O75445 usherin Enzyme modulator 119 0.579 0.692 1.6E-94 0.100 None 0 1
Entrez Id: 9381
Gene Symbol: OTOF
OTOF
Q9HC10 otoferlin Transporter 34 0.691 0.385 5.4E-39 0.400 None 1.000 1 2 2007 2007
Entrez Id: 4647
Gene Symbol: MYO7A
MYO7A
Q13402 myosin VIIA Cellular structure 104 0.585 0.423 1.6E-38 0.300 None 1.000 1 5 2005 2005
Entrez Id: 340990
Gene Symbol: OTOG
OTOG
Q6ZRI0 otogelin 10 0.805 0.231 6.6E-37 0.100 None 0 1
Entrez Id: 125336
Gene Symbol: LOXHD1
LOXHD1
Q8IVV2 lipoxygenase homology domains 1 11 0.792 0.231 5.6E-26 0.100 None 0 1
Entrez Id: 65217
Gene Symbol: PCDH15
PCDH15
Q96QU1 protocadherin related 15 94 0.601 0.577 8.0E-25 0.310 None 1.000 2 0 2000 2008
Entrez Id: 254268
Gene Symbol: AKNAD1
AKNAD1
Q5T1N1 AKNA domain containing 1 9 0.890 0.269 3.6E-23 0.100 None 0 1
Entrez Id: 5172
Gene Symbol: SLC26A4
SLC26A4
O43511 solute carrier family 26 member 4 Transporter 194 0.507 0.885 9.0E-22 0.100 None 0 4
Entrez Id: 374462
Gene Symbol: PTPRQ
PTPRQ
Q9UMZ3 protein tyrosine phosphatase receptor type Q 21 0.751 0.462 4.2E-21 0.100 None 0 2
Entrez Id: 117531
Gene Symbol: TMC1
TMC1
Q8TDI8 transmembrane channel like 1 Ion channel 16 0.769 0.346 9.2E-19 0.100 None 0 4
Entrez Id: 10723
Gene Symbol: SLC12A7
SLC12A7
Q9Y666 solute carrier family 12 member 7 Transporter 31 0.769 0.385 1.4E-17 0.010 None 1.000 1 0 2002 2002
Entrez Id: 1187
Gene Symbol: CLCNKA
CLCNKA
P51800 chloride voltage-gated channel Ka Ion channel 37 0.711 0.385 4.2E-17 0.100 None 0 1
Entrez Id: 7007
Gene Symbol: TECTA
TECTA
O75443 tectorin alpha 24 0.700 0.385 3.0E-16 0.100 None 0 1
Entrez Id: 2706
Gene Symbol: GJB2
GJB2
P29033 gap junction protein beta 2 Cell-cell junction 392 0.441 0.846 6.6E-16 0.450 None 1.000 6 1 2002 2008
Entrez Id: 83959
Gene Symbol: SLC4A11
SLC4A11
Q8NBS3 solute carrier family 4 member 11 Transporter 42 0.674 0.385 4.6E-15 0.010 None 1.000 1 0 2002 2002
Entrez Id: 153562
Gene Symbol: MARVELD2
MARVELD2
Q8N4S9 MARVEL domain containing 2 Cell-cell junction 26 0.705 0.462 1.3E-12 0.100 None 0 1
Entrez Id: 286676
Gene Symbol: ILDR1
ILDR1
Q86SU0 immunoglobulin like domain containing receptor 1 20 0.729 0.346 2.6E-12 0.100 None 0 1
Entrez Id: 389207
Gene Symbol: GRXCR1
GRXCR1
A8MXD5 glutaredoxin and cysteine rich domain containing 1 9 0.861 0.115 3.9E-11 0.100 None 0 1
Entrez Id: 64699
Gene Symbol: TMPRSS3
TMPRSS3
P57727 transmembrane serine protease 3 Enzyme 45 0.650 0.538 6.1E-11 0.010 None 1.000 1 0 2004 2004
Entrez Id: 345895
Gene Symbol: RSPH4A
RSPH4A
Q5TD94 radial spoke head component 4A 57 0.666 0.538 7.6E-11 0.300 None 1.000 1 0 2015 2015
Entrez Id: 29899
Gene Symbol: GPSM2
GPSM2
P81274 G protein signaling modulator 2 38 0.682 0.538 7.7E-11 0.100 None 0 1
Entrez Id: 7809
Gene Symbol: BSND
BSND
Q8WZ55 barttin CLCNK type accessory subunit beta 91 0.603 0.692 1.1E-10 0.020 None 1.000 2 0 2006 2006
Entrez Id: 83715
Gene Symbol: ESPN
ESPN
B1AK53 espin Cellular structure 28 0.700 0.385 2.9E-09 0.300 None 1.000 2 0 2004 2006