Entrez Id: |
379003 |
Gene Symbol: |
DFNB40 |
DFNB40
|
|
deafness, autosomal recessive 40
|
|
1
|
1.000 |
0.115 |
|
0.010 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
1713 |
Gene Symbol: |
DFNB20 |
DFNB20
|
|
deafness, autosomal recessive 20
|
|
2
|
1.000 |
0.115 |
|
0.010 |
None
|
1.000 |
1
|
0
|
1999 |
1999 |
Entrez Id: |
26297 |
Gene Symbol: |
SERGEF |
SERGEF
|
Q9UGK8
|
secretion regulating guanine nucleotide exchange factor
|
|
2
|
1.000 |
0.115 |
5.3E-14 |
0.010 |
None
|
1.000 |
1
|
0
|
1999 |
1999 |
Entrez Id: |
347713 |
Gene Symbol: |
DFNA42 |
DFNA42
|
|
deafness, autosomal dominant 42
|
|
2
|
0.931 |
0.115 |
|
0.010 |
None
|
1.000 |
1
|
0
|
2008 |
2008 |
Entrez Id: |
448962 |
Gene Symbol: |
DFNA54 |
DFNA54
|
|
deafness, autosomal dominant 54
|
|
2
|
0.931 |
0.115 |
|
0.010 |
None
|
1.000 |
1
|
0
|
2006 |
2006 |
Entrez Id: |
23262 |
Gene Symbol: |
PPIP5K2 |
PPIP5K2
|
O43314
|
diphosphoinositol pentakisphosphate kinase 2
|
|
4
|
0.890 |
0.154 |
8.6E-21 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
1680 |
Gene Symbol: |
DFNX3 |
DFNX3
|
|
deafness, X-linked 3
|
|
5
|
0.861 |
0.192 |
|
0.010 |
None
|
1.000 |
1
|
0
|
1998 |
1998 |
Entrez Id: |
259236 |
Gene Symbol: |
TMIE |
TMIE
|
Q8NEW7
|
transmembrane inner ear
|
|
5
|
0.890 |
0.115 |
7.7E-05 |
0.010 |
None
|
1.000 |
1
|
0
|
1995 |
1995 |
Entrez Id: |
9080 |
Gene Symbol: |
CLDN9 |
CLDN9
|
O95484
|
claudin 9
|
Cell-cell junction
|
5
|
0.861 |
0.231 |
6.3E-06 |
0.010 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
TMEM132E
|
Q6IEE7
|
transmembrane protein 132E
|
|
7
|
0.805 |
0.231 |
4.5E-05 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
286262 |
Gene Symbol: |
TPRN |
TPRN
|
Q4KMQ1
|
taperin
|
|
7
|
0.839 |
0.115 |
7.2E-03 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
9885 |
Gene Symbol: |
OSBPL2 |
OSBPL2
|
Q9H1P3
|
oxysterol binding protein like 2
|
|
7
|
0.861 |
0.154 |
0.13 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
10750 |
Gene Symbol: |
GRAP |
GRAP
|
Q13588
|
GRB2 related adaptor protein
|
|
8
|
0.821 |
0.462 |
0.11 |
0.110 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
283310 |
Gene Symbol: |
OTOGL |
OTOGL
|
Q3ZCN5
|
otogelin like
|
Enzyme modulator
|
9
|
0.805 |
0.269 |
4.7E-52 |
0.030 |
None
|
1.000 |
3
|
2
|
2012 |
2017 |
Entrez Id: |
220074 |
Gene Symbol: |
LRTOMT |
LRTOMT
|
Q8WZ04 Q96E66
|
leucine rich transmembrane and O-methyltransferase domain containing
|
Enzyme
|
9
|
0.792 |
0.192 |
7.0E-05 |
0.300 |
strong
|
1.000 |
1
|
0
|
2008 |
2008 |
Entrez Id: |
389207 |
Gene Symbol: |
GRXCR1 |
GRXCR1
|
A8MXD5
|
glutaredoxin and cysteine rich domain containing 1
|
|
9
|
0.861 |
0.115 |
3.9E-11 |
0.010 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
Entrez Id: |
60526 |
Gene Symbol: |
LDAH |
LDAH
|
Q9H6V9
|
lipid droplet associated hydrolase
|
|
9
|
0.839 |
0.231 |
3.6E-04 |
0.010 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
CEACAM16
|
Q2WEN9
|
CEA cell adhesion molecule 16, tectorial membrane component
|
|
10
|
0.805 |
0.192 |
1.6E-05 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
51116 |
Gene Symbol: |
MRPS2 |
MRPS2
|
Q9Y399
|
mitochondrial ribosomal protein S2
|
Nucleic acid binding
|
11
|
0.839 |
0.154 |
3.1E-07 |
0.110 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
Entrez Id: |
53904 |
Gene Symbol: |
MYO3A |
MYO3A
|
Q8NEV4
|
myosin IIIA
|
Kinase
|
11
|
0.780 |
0.269 |
1.8E-45 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
CATSPER2
|
Q96P56
|
cation channel sperm associated 2
|
Ion channel
|
11
|
0.805 |
0.154 |
5.9E-17 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
53405 |
Gene Symbol: |
CLIC5 |
CLIC5
|
Q9NZA1
|
chloride intracellular channel 5
|
Ion channel
|
11
|
0.792 |
0.308 |
1.6E-06 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
126326 |
Gene Symbol: |
GIPC3 |
GIPC3
|
Q8TF64
|
GIPC PDZ domain containing family member 3
|
Enzyme
|
12
|
0.780 |
0.231 |
9.3E-03 |
0.140 |
None
|
1.000 |
4
|
1
|
2011 |
2018 |
Entrez Id: |
146183 |
Gene Symbol: |
OTOA |
OTOA
|
Q7RTW8
|
otoancorin
|
Extracellular structure
|
12
|
0.760 |
0.423 |
3.0E-10 |
0.110 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
9015 |
Gene Symbol: |
TAF1A |
TAF1A
|
Q15573
|
TATA-box binding protein associated factor, RNA polymerase I subunit A
|
|
12
|
0.805 |
0.308 |
1.2E-09 |
0.100 |
None
|
|
0
|
0
|
|
|