Entrez Id: |
2232 |
Gene Symbol: |
FDXR |
FDXR
|
P22570
|
ferredoxin reductase
|
Enzyme
|
103
|
0.566 |
0.808 |
1.1E-06 |
0.110 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
7345 |
Gene Symbol: |
UCHL1 |
UCHL1
|
P09936
|
ubiquitin C-terminal hydrolase L1
|
Enzyme
|
260
|
0.482 |
0.885 |
0.99 |
0.110 |
None
|
1.000 |
1
|
0
|
2015 |
2015 |
Entrez Id: |
1201 |
Gene Symbol: |
CLN3 |
CLN3
|
Q13286
|
CLN3 lysosomal/endosomal transmembrane protein, battenin
|
Transporter
|
120
|
0.572 |
0.692 |
1.3E-07 |
0.110 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
8086 |
Gene Symbol: |
AAAS |
AAAS
|
Q9NRG9
|
aladin WD repeat nucleoporin
|
|
92
|
0.601 |
0.654 |
2.4E-13 |
0.110 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
Entrez Id: |
28962 |
Gene Symbol: |
OSTM1 |
OSTM1
|
Q86WC4
|
osteoclastogenesis associated transmembrane protein 1
|
|
66
|
0.644 |
0.577 |
1.1E-02 |
0.110 |
None
|
1.000 |
1
|
0
|
2006 |
2006 |
Entrez Id: |
773 |
Gene Symbol: |
CACNA1A |
CACNA1A
|
O00555
|
calcium voltage-gated channel subunit alpha1 A
|
Ion channel
|
320
|
0.489 |
0.769 |
1.00 |
0.110 |
None
|
1.000 |
1
|
0
|
2016 |
2016 |
Entrez Id: |
1678 |
Gene Symbol: |
TIMM8A |
TIMM8A
|
O60220
|
translocase of inner mitochondrial membrane 8A
|
|
200
|
0.510 |
0.846 |
0.65 |
0.110 |
None
|
1.000 |
1
|
0
|
2009 |
2009 |
Entrez Id: |
4535 |
Gene Symbol: |
ND1 |
ND1
|
P03886
|
NADH dehydrogenase, subunit 1 (complex I)
|
Enzyme
|
260
|
0.522 |
0.769 |
|
0.110 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
10730 |
Gene Symbol: |
YME1L1 |
YME1L1
|
Q96TA2
|
YME1 like 1 ATPase
|
Enzyme
|
60
|
0.633 |
0.654 |
2.9E-02 |
0.110 |
None
|
1.000 |
1
|
0
|
2016 |
2016 |
Entrez Id: |
6687 |
Gene Symbol: |
SPG7 |
SPG7
|
Q9UQ90
|
SPG7 matrix AAA peptidase subunit, paraplegin
|
Enzyme
|
419
|
0.436 |
0.885 |
2.0E-36 |
0.110 |
None
|
1.000 |
1
|
0
|
2009 |
2009 |
Entrez Id: |
51218 |
Gene Symbol: |
GLRX5 |
GLRX5
|
Q86SX6
|
glutaredoxin 5
|
Enzyme
|
70
|
0.659 |
0.538 |
0.75 |
0.110 |
None
|
1.000 |
1
|
0
|
2014 |
2014 |
Entrez Id: |
478 |
Gene Symbol: |
ATP1A3 |
ATP1A3
|
P13637
|
ATPase Na+/K+ transporting subunit alpha 3
|
Transporter
|
174
|
0.544 |
0.615 |
1.00 |
0.110 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
Entrez Id: |
6389 |
Gene Symbol: |
SDHA |
SDHA
|
P31040
|
succinate dehydrogenase complex flavoprotein subunit A
|
Enzyme
|
246
|
0.517 |
0.731 |
2.6E-10 |
0.110 |
None
|
< 0.001 |
1
|
0
|
2005 |
2005 |
Entrez Id: |
79581 |
Gene Symbol: |
SLC52A2 |
SLC52A2
|
Q9HAB3
|
solute carrier family 52 member 2
|
Transporter
|
261
|
0.483 |
0.808 |
2.5E-03 |
0.110 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
Entrez Id: |
51102 |
Gene Symbol: |
MECR |
MECR
|
Q9BV79
|
mitochondrial trans-2-enoyl-CoA reductase
|
|
29
|
0.736 |
0.385 |
2.2E-05 |
0.110 |
None
|
1.000 |
1
|
6
|
2016 |
2016 |
Entrez Id: |
5631 |
Gene Symbol: |
PRPS1 |
PRPS1
|
P60891
|
phosphoribosyl pyrophosphate synthetase 1
|
Kinase
|
151
|
0.584 |
0.731 |
0.92 |
0.110 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
56947 |
Gene Symbol: |
MFF |
MFF
|
Q9GZY8
|
mitochondrial fission factor
|
|
44
|
0.705 |
0.462 |
6.5E-02 |
0.110 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
10312 |
Gene Symbol: |
TCIRG1 |
TCIRG1
|
Q13488
|
T cell immune regulator 1, ATPase H+ transporting V0 subunit a3
|
Transporter
|
146
|
0.565 |
0.692 |
2.4E-13 |
0.110 |
None
|
1.000 |
1
|
0
|
2006 |
2006 |
Entrez Id: |
92609 |
Gene Symbol: |
TIMM50 |
TIMM50
|
Q3ZCQ8
|
translocase of inner mitochondrial membrane 50
|
|
50
|
0.678 |
0.500 |
1.8E-03 |
0.110 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
2395 |
Gene Symbol: |
FXN |
FXN
|
Q16595
|
frataxin
|
Enzyme
|
220
|
0.510 |
0.654 |
0.34 |
0.110 |
None
|
1.000 |
1
|
0
|
2009 |
2009 |
Entrez Id: |
6310 |
Gene Symbol: |
ATXN1 |
ATXN1
|
P54253
|
ataxin 1
|
|
218
|
0.534 |
0.769 |
0.97 |
0.110 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
4724 |
Gene Symbol: |
NDUFS4 |
NDUFS4
|
O43181
|
NADH:ubiquinone oxidoreductase subunit S4
|
|
137
|
0.587 |
0.808 |
3.1E-04 |
0.110 |
None
|
< 0.001 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
6314 |
Gene Symbol: |
ATXN7 |
ATXN7
|
O15265
|
ataxin 7
|
|
162
|
0.581 |
0.654 |
0.96 |
0.110 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
8506 |
Gene Symbol: |
CNTNAP1 |
CNTNAP1
|
P78357
|
contactin associated protein 1
|
|
166
|
0.554 |
0.577 |
3.4E-05 |
0.100 |
None
|
1.000 |
1
|
1
|
2017 |
2017 |
Entrez Id: |
57096 |
Gene Symbol: |
RPGRIP1 |
RPGRIP1
|
Q96KN7
|
RPGR interacting protein 1
|
Enzyme modulator
|
121
|
0.553 |
0.654 |
1.3E-23 |
0.100 |
None
|
|
0
|
0
|
|
|