Entrez Id: |
1200 |
Gene Symbol: |
TPP1 |
TPP1
|
O14773
|
tripeptidyl peptidase 1
|
Enzyme
|
151
|
0.551 |
0.808 |
6.3E-07 |
0.040 |
None
|
1.000 |
4
|
0
|
1999 |
2019 |
Entrez Id: |
9374 |
Gene Symbol: |
PPT2 |
PPT2
|
Q9UMR5
|
palmitoyl-protein thioesterase 2
|
Enzyme
|
27
|
0.751 |
0.500 |
4.5E-03 |
0.020 |
None
|
1.000 |
2
|
0
|
1999 |
2003 |
Entrez Id: |
1201 |
Gene Symbol: |
CLN3 |
CLN3
|
Q13286
|
CLN3 lysosomal/endosomal transmembrane protein, battenin
|
Transporter
|
120
|
0.572 |
0.692 |
1.3E-07 |
0.100 |
None
|
1.000 |
13
|
0
|
2000 |
2019 |
Entrez Id: |
1508 |
Gene Symbol: |
CTSB |
CTSB
|
P07858
|
cathepsin B
|
Enzyme
|
304
|
0.457 |
0.846 |
5.9E-11 |
0.030 |
None
|
1.000 |
3
|
0
|
2000 |
2019 |
Entrez Id: |
57192 |
Gene Symbol: |
MCOLN1 |
MCOLN1
|
Q9GZU1
|
mucolipin 1
|
Ion channel
|
102
|
0.601 |
0.654 |
5.8E-04 |
0.100 |
None
|
0.955 |
22
|
0
|
2001 |
2019 |
Entrez Id: |
1497 |
Gene Symbol: |
CTNS |
CTNS
|
O60931
|
cystinosin, lysosomal cystine transporter
|
|
88
|
0.628 |
0.538 |
3.1E-04 |
0.080 |
None
|
0.750 |
8
|
0
|
2001 |
2019 |
Entrez Id: |
3988 |
Gene Symbol: |
LIPA |
LIPA
|
P38571
|
lipase A, lysosomal acid type
|
Enzyme
|
130
|
0.564 |
0.654 |
5.5E-07 |
0.020 |
None
|
1.000 |
2
|
0
|
2001 |
2017 |
Entrez Id: |
4126 |
Gene Symbol: |
MANBA |
MANBA
|
O00462
|
mannosidase beta
|
Enzyme
|
38
|
0.736 |
0.462 |
1.3E-18 |
0.030 |
None
|
1.000 |
3
|
0
|
2002 |
2015 |
Entrez Id: |
7157 |
Gene Symbol: |
TP53 |
TP53
|
P04637
|
tumor protein p53
|
Transcription factor
|
2494
|
0.236 |
0.962 |
0.53 |
0.010 |
None
|
1.000 |
1
|
0
|
2002 |
2002 |
Entrez Id: |
5660 |
Gene Symbol: |
PSAP |
PSAP
|
P07602
|
prosaposin
|
|
189
|
0.532 |
0.846 |
0.99 |
0.040 |
None
|
1.000 |
4
|
0
|
2003 |
2017 |
Entrez Id: |
696 |
Gene Symbol: |
BTN1A1 |
BTN1A1
|
Q13410
|
butyrophilin subfamily 1 member A1
|
Enzyme modulator
|
9
|
0.839 |
0.346 |
1.9E-08 |
0.010 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
3073 |
Gene Symbol: |
HEXA |
HEXA
|
P06865
|
hexosaminidase subunit alpha
|
Enzyme
|
79
|
0.633 |
0.615 |
1.3E-11 |
0.040 |
None
|
1.000 |
4
|
0
|
2004 |
2019 |
Entrez Id: |
2799 |
Gene Symbol: |
GNS |
GNS
|
P15586
|
glucosamine (N-acetyl)-6-sulfatase
|
Enzyme
|
51
|
0.705 |
0.538 |
5.6E-04 |
0.020 |
None
|
1.000 |
2
|
0
|
2004 |
2017 |
Entrez Id: |
858 |
Gene Symbol: |
CAV2 |
CAV2
|
P51636
|
caveolin 2
|
Enzyme modulator
|
96
|
0.575 |
0.692 |
2.7E-02 |
0.020 |
None
|
1.000 |
2
|
0
|
2004 |
2014 |
Entrez Id: |
1999 |
Gene Symbol: |
ELF3 |
ELF3
|
P78545
|
E74 like ETS transcription factor 3
|
Transcription factor
|
112
|
0.551 |
0.808 |
0.98 |
0.020 |
None
|
1.000 |
2
|
0
|
2004 |
2016 |
Entrez Id: |
3074 |
Gene Symbol: |
HEXB |
HEXB
|
P07686
|
hexosaminidase subunit beta
|
Enzyme
|
62
|
0.644 |
0.654 |
3.5E-10 |
0.010 |
None
|
1.000 |
1
|
0
|
2004 |
2004 |
Entrez Id: |
54982 |
Gene Symbol: |
CLN6 |
CLN6
|
Q9NWW5
|
CLN6 transmembrane ER protein
|
|
59
|
0.670 |
0.231 |
1.0E-04 |
0.010 |
None
|
1.000 |
1
|
0
|
2004 |
2004 |
Entrez Id: |
7422 |
Gene Symbol: |
VEGFA |
VEGFA
|
P15692
|
vascular endothelial growth factor A
|
Signaling
|
1899
|
0.266 |
0.923 |
2.4E-05 |
0.010 |
None
|
1.000 |
1
|
0
|
2004 |
2004 |
Entrez Id: |
947 |
Gene Symbol: |
CD34 |
CD34
|
P28906
|
CD34 molecule
|
|
674
|
0.368 |
0.808 |
5.0E-06 |
0.010 |
None
|
1.000 |
1
|
0
|
2004 |
2004 |
Entrez Id: |
26503 |
Gene Symbol: |
SLC17A5 |
SLC17A5
|
Q9NRA2
|
solute carrier family 17 member 5
|
Transporter
|
252
|
0.491 |
0.808 |
6.9E-10 |
0.210 |
None
|
1.000 |
1
|
0
|
2004 |
2004 |
Entrez Id: |
2720 |
Gene Symbol: |
GLB1 |
GLB1
|
P16278
|
galactosidase beta 1
|
Enzyme
|
385
|
0.448 |
0.808 |
7.9E-10 |
0.100 |
None
|
0.917 |
12
|
1
|
2005 |
2019 |
Entrez Id: |
4669 |
Gene Symbol: |
NAGLU |
NAGLU
|
P54802
|
N-acetyl-alpha-glucosaminidase
|
|
152
|
0.546 |
0.769 |
1.4E-08 |
0.080 |
None
|
1.000 |
8
|
1
|
2005 |
2019 |
Entrez Id: |
1118 |
Gene Symbol: |
CHIT1 |
CHIT1
|
Q13231
|
chitinase 1
|
|
142
|
0.525 |
0.692 |
7.2E-16 |
0.060 |
None
|
1.000 |
6
|
0
|
2005 |
2018 |
Entrez Id: |
1186 |
Gene Symbol: |
CLCN7 |
CLCN7
|
P51798
|
chloride voltage-gated channel 7
|
Ion channel
|
135
|
0.590 |
0.731 |
0.27 |
0.020 |
None
|
1.000 |
2
|
0
|
2005 |
2012 |
Entrez Id: |
2581 |
Gene Symbol: |
GALC |
GALC
|
P54803
|
galactosylceramidase
|
|
99
|
0.604 |
0.615 |
5.2E-15 |
0.070 |
None
|
1.000 |
7
|
0
|
2006 |
2019 |