Entrez Id: |
6834 |
Gene Symbol: |
SURF1 |
SURF1
|
Q15526
|
SURF1 cytochrome c oxidase assembly factor
|
Enzyme
|
150
|
0.578 |
0.654 |
1.6E-13 |
0.010 |
None
|
1.000 |
1
|
0
|
2016 |
2016 |
Entrez Id: |
8086 |
Gene Symbol: |
AAAS |
AAAS
|
Q9NRG9
|
aladin WD repeat nucleoporin
|
|
92
|
0.601 |
0.654 |
2.4E-13 |
0.010 |
None
|
1.000 |
1
|
1
|
2008 |
2008 |
Entrez Id: |
5376 |
Gene Symbol: |
PMP22 |
PMP22
|
Q01453
|
peripheral myelin protein 22
|
Cellular structure
|
341
|
0.471 |
0.885 |
0.91 |
0.010 |
None
|
1.000 |
1
|
1
|
2011 |
2011 |
Entrez Id: |
5354 |
Gene Symbol: |
PLP1 |
PLP1
|
P60201
|
proteolipid protein 1
|
Cellular structure
|
160
|
0.543 |
0.769 |
0.93 |
0.010 |
None
|
1.000 |
1
|
0
|
2006 |
2006 |
Entrez Id: |
5165 |
Gene Symbol: |
PDK3 |
PDK3
|
Q15120
|
pyruvate dehydrogenase kinase 3
|
Kinase
|
51
|
0.678 |
0.500 |
0.45 |
0.010 |
None
|
1.000 |
1
|
1
|
2016 |
2016 |
Entrez Id: |
8988 |
Gene Symbol: |
HSPB3 |
HSPB3
|
Q12988
|
heat shock protein family B (small) member 3
|
|
327
|
0.448 |
0.769 |
6.1E-05 |
0.010 |
None
|
1.000 |
1
|
0
|
2015 |
2015 |
Entrez Id: |
4771 |
Gene Symbol: |
NF2 |
NF2
|
P35240
|
neurofibromin 2
|
|
312
|
0.468 |
0.885 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
56652 |
Gene Symbol: |
TWNK |
TWNK
|
Q96RR1
|
twinkle mtDNA helicase
|
Enzyme
|
245
|
0.516 |
0.692 |
3.2E-03 |
0.010 |
None
|
1.000 |
1
|
0
|
2004 |
2004 |
Entrez Id: |
9131 |
Gene Symbol: |
AIFM1 |
AIFM1
|
O95831
|
apoptosis inducing factor mitochondria associated 1
|
Enzyme
|
205
|
0.527 |
0.769 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
1996 |
1996 |
Entrez Id: |
80208 |
Gene Symbol: |
SPG11 |
SPG11
|
Q96JI7
|
SPG11 vesicle trafficking associated, spatacsin
|
|
139
|
0.576 |
0.538 |
1.6E-39 |
0.010 |
None
|
1.000 |
1
|
0
|
2016 |
2016 |
Entrez Id: |
79594 |
Gene Symbol: |
MUL1 |
MUL1
|
Q969V5
|
mitochondrial E3 ubiquitin protein ligase 1
|
|
241
|
0.473 |
0.808 |
1.9E-06 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
6305 |
Gene Symbol: |
SBF1 |
SBF1
|
O95248
|
SET binding factor 1
|
Enzyme
|
34
|
0.700 |
0.500 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
7150 |
Gene Symbol: |
TOP1 |
TOP1
|
P11387
|
DNA topoisomerase I
|
Enzyme
|
143
|
0.542 |
0.692 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
2014 |
2014 |
Entrez Id: |
56704 |
Gene Symbol: |
JPH1 |
JPH1
|
Q9HDC5
|
junctophilin 1
|
|
29
|
0.705 |
0.269 |
0.77 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
7347 |
Gene Symbol: |
UCHL3 |
UCHL3
|
P15374
|
ubiquitin C-terminal hydrolase L3
|
Enzyme
|
24
|
0.705 |
0.385 |
3.3E-08 |
0.010 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
C12orf65
|
Q9H3J6
|
chromosome 12 open reading frame 65
|
Nucleic acid binding
|
65
|
0.678 |
0.346 |
0.21 |
0.010 |
None
|
1.000 |
1
|
0
|
2014 |
2014 |
Entrez Id: |
55210 |
Gene Symbol: |
ATAD3A |
ATAD3A
|
Q9NVI7
|
ATPase family AAA domain containing 3A
|
Enzyme
|
81
|
0.628 |
0.692 |
4.1E-09 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
54840 |
Gene Symbol: |
APTX |
APTX
|
Q7Z2E3
|
aprataxin
|
Nucleic acid binding
|
94
|
0.590 |
0.500 |
4.0E-10 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
547 |
Gene Symbol: |
KIF1A |
KIF1A
|
Q12756
|
kinesin family member 1A
|
Cellular structure
|
187
|
0.559 |
0.692 |
1.00 |
0.010 |
None
|
1.000 |
1
|
1
|
2017 |
2017 |
Entrez Id: |
8898 |
Gene Symbol: |
MTMR2 |
MTMR2
|
Q13614
|
myotubularin related protein 2
|
Enzyme
|
50
|
0.659 |
0.538 |
3.0E-07 |
0.010 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
4358 |
Gene Symbol: |
MPV17 |
MPV17
|
P39210
|
mitochondrial inner membrane protein MPV17
|
Receptor
|
134
|
0.595 |
0.577 |
9.7E-11 |
0.010 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
23321 |
Gene Symbol: |
TRIM2 |
TRIM2
|
Q9C040
|
tripartite motif containing 2
|
Enzyme
|
44
|
0.686 |
0.538 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
538 |
Gene Symbol: |
ATP7A |
ATP7A
|
Q04656
|
ATPase copper transporting alpha
|
Transporter
|
348
|
0.494 |
0.769 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
2015 |
2015 |
Entrez Id: |
23064 |
Gene Symbol: |
SETX |
SETX
|
Q7Z333
|
senataxin
|
Enzyme
|
133
|
0.570 |
0.731 |
0.95 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
26353 |
Gene Symbol: |
HSPB8 |
HSPB8
|
Q9UJY1
|
heat shock protein family B (small) member 8
|
|
122
|
0.570 |
0.577 |
4.3E-02 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |