Entrez Id: |
54931 |
Gene Symbol: |
TRMT10C |
TRMT10C
|
Q7L0Y3
|
tRNA methyltransferase 10C, mitochondrial RNase P subunit
|
|
14
|
0.839 |
0.154 |
9.7E-05 |
0.010 |
None
|
1.000 |
1
|
0
|
2016 |
2016 |
Entrez Id: |
11222 |
Gene Symbol: |
MRPL3 |
MRPL3
|
P09001
|
mitochondrial ribosomal protein L3
|
|
15
|
0.792 |
0.192 |
1.3E-12 |
0.010 |
None
|
1.000 |
1
|
0
|
2011 |
2011 |
Entrez Id: |
57570 |
Gene Symbol: |
TRMT5 |
TRMT5
|
Q32P41
|
tRNA methyltransferase 5
|
Enzyme
|
28
|
0.769 |
0.231 |
5.0E-02 |
0.010 |
None
|
1.000 |
1
|
0
|
2015 |
2015 |
Entrez Id: |
60528 |
Gene Symbol: |
ELAC2 |
ELAC2
|
Q9BQ52
|
elaC ribonuclease Z 2
|
|
40
|
0.670 |
0.346 |
1.7E-20 |
0.010 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
55687 |
Gene Symbol: |
TRMU |
TRMU
|
O75648
|
tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
|
|
50
|
0.716 |
0.385 |
1.5E-16 |
0.020 |
None
|
1.000 |
2
|
0
|
2013 |
2019 |
Entrez Id: |
54902 |
Gene Symbol: |
TTC19 |
TTC19
|
Q6DKK2
|
tetratricopeptide repeat domain 19
|
|
78
|
0.663 |
0.385 |
1.4E-08 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
26235 |
Gene Symbol: |
FBXL4 |
FBXL4
|
Q9UKA2
|
F-box and leucine rich repeat protein 4
|
|
55
|
0.695 |
0.423 |
1.1E-08 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
80224 |
Gene Symbol: |
NUBPL |
NUBPL
|
Q8TB37
|
nucleotide binding protein like
|
|
77
|
0.670 |
0.423 |
1.1E-05 |
0.300 |
None
|
1.000 |
1
|
0
|
2010 |
2010 |
Entrez Id: |
92667 |
Gene Symbol: |
MGME1 |
MGME1
|
Q9BQP7
|
mitochondrial genome maintenance exonuclease 1
|
|
52
|
0.695 |
0.423 |
1.8E-03 |
0.300 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
25821 |
Gene Symbol: |
MTO1 |
MTO1
|
Q9Y2Z2
|
mitochondrial tRNA translation optimization 1
|
|
48
|
0.670 |
0.462 |
7.4E-06 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
55572 |
Gene Symbol: |
FOXRED1 |
FOXRED1
|
Q96CU9
|
FAD dependent oxidoreductase domain containing 1
|
Enzyme
|
91
|
0.633 |
0.462 |
2.0E-16 |
0.300 |
None
|
1.000 |
1
|
0
|
2010 |
2010 |
Entrez Id: |
57038 |
Gene Symbol: |
RARS2 |
RARS2
|
Q5T160
|
arginyl-tRNA synthetase 2, mitochondrial
|
|
57
|
0.663 |
0.462 |
7.7E-14 |
0.010 |
None
|
1.000 |
1
|
0
|
2015 |
2015 |
Entrez Id: |
87178 |
Gene Symbol: |
PNPT1 |
PNPT1
|
Q8TCS8
|
polyribonucleotide nucleotidyltransferase 1
|
Enzyme
|
64
|
0.653 |
0.462 |
4.0E-04 |
0.010 |
None
|
1.000 |
1
|
0
|
2012 |
2012 |
Entrez Id: |
1716 |
Gene Symbol: |
DGUOK |
DGUOK
|
Q16854
|
deoxyguanosine kinase
|
Kinase
|
112
|
0.593 |
0.500 |
3.7E-07 |
0.020 |
None
|
1.000 |
2
|
0
|
2005 |
2009 |
Entrez Id: |
57505 |
Gene Symbol: |
AARS2 |
AARS2
|
Q5JTZ9
|
alanyl-tRNA synthetase 2, mitochondrial
|
Nucleic acid binding
|
64
|
0.644 |
0.500 |
5.0E-17 |
0.010 |
None
|
1.000 |
1
|
0
|
2011 |
2011 |
Entrez Id: |
23082 |
Gene Symbol: |
PPRC1 |
PPRC1
|
Q5VV67
|
PPARG related coactivator 1
|
Transcription factor
|
41
|
0.656 |
0.538 |
1.00 |
0.010 |
None
|
1.000 |
1
|
0
|
2009 |
2009 |
Entrez Id: |
4358 |
Gene Symbol: |
MPV17 |
MPV17
|
P39210
|
mitochondrial inner membrane protein MPV17
|
Receptor
|
134
|
0.595 |
0.577 |
9.7E-11 |
0.300 |
None
|
1.000 |
1
|
0
|
2009 |
2009 |
Entrez Id: |
51204 |
Gene Symbol: |
TACO1 |
TACO1
|
Q9BSH4
|
translational activator of cytochrome c oxidase I
|
|
70
|
0.647 |
0.577 |
1.5E-03 |
0.010 |
None
|
1.000 |
1
|
0
|
2010 |
2010 |
Entrez Id: |
55157 |
Gene Symbol: |
DARS2 |
DARS2
|
Q6PI48
|
aspartyl-tRNA synthetase 2, mitochondrial
|
Enzyme
|
92
|
0.638 |
0.577 |
9.8E-13 |
0.010 |
None
|
1.000 |
1
|
0
|
2017 |
2017 |
Entrez Id: |
1892 |
Gene Symbol: |
ECHS1 |
ECHS1
|
P30084
|
enoyl-CoA hydratase, short chain 1
|
Enzyme
|
93
|
0.601 |
0.654 |
8.8E-04 |
0.010 |
None
|
1.000 |
1
|
0
|
2015 |
2015 |
Entrez Id: |
2395 |
Gene Symbol: |
FXN |
FXN
|
Q16595
|
frataxin
|
Enzyme
|
220
|
0.510 |
0.654 |
0.34 |
0.010 |
None
|
1.000 |
1
|
0
|
2011 |
2011 |
Entrez Id: |
51196 |
Gene Symbol: |
PLCE1 |
PLCE1
|
Q9P212
|
phospholipase C epsilon 1
|
Enzyme
|
114
|
0.572 |
0.654 |
5.7E-11 |
0.010 |
None
|
1.000 |
1
|
0
|
2011 |
2011 |
Entrez Id: |
80308 |
Gene Symbol: |
FLAD1 |
FLAD1
|
Q8NFF5
|
flavin adenine dinucleotide synthetase 1
|
|
58
|
0.638 |
0.692 |
9.4E-03 |
0.030 |
None
|
1.000 |
3
|
0
|
2016 |
2019 |
Entrez Id: |
10667 |
Gene Symbol: |
FARS2 |
FARS2
|
O95363
|
phenylalanyl-tRNA synthetase 2, mitochondrial
|
Enzyme
|
89
|
0.615 |
0.731 |
9.3E-09 |
0.010 |
None
|
1.000 |
1
|
1
|
2014 |
2014 |
Entrez Id: |
4575 |
Gene Symbol: |
TRNS2 |
TRNS2
|
|
tRNA
|
|
152
|
0.579 |
0.731 |
|
0.010 |
None
|
1.000 |
1
|
0
|
2012 |
2012 |