Gene UniProt Gene Full Name Protein Class N. diseases g DSI g DPI g pLI Score gda EL gda EI gda N. PMIDs N. SNPs gda First Ref. Last Ref.
Entrez Id: 51168
Gene Symbol: MYO15A
MYO15A
Q9UKN7 myosin XVA Cellular structure 26 0.722 0.346 1.3E-56 0.020 None 1.000 2 0 1999 2019
Entrez Id: 9381
Gene Symbol: OTOF
OTOF
Q9HC10 otoferlin Transporter 34 0.691 0.385 5.4E-39 0.140 None 1.000 5 1 2002 2016
Entrez Id: 11078
Gene Symbol: TRIOBP
TRIOBP
Q9H2D6 TRIO and F-actin binding protein Enzyme modulator 25 0.743 0.269 2.0E-28 0.300 definitive 1.000 8 0 2006 2016
Entrez Id: 5172
Gene Symbol: SLC26A4
SLC26A4
O43511 solute carrier family 26 member 4 Transporter 194 0.507 0.885 9.0E-22 0.040 None 1.000 4 0 2013 2019
Entrez Id: 374462
Gene Symbol: PTPRQ
PTPRQ
Q9UMZ3 protein tyrosine phosphatase receptor type Q 21 0.751 0.462 4.2E-21 0.300 definitive 1.000 8 0 2003 2015
Entrez Id: 84173
Gene Symbol: ELMOD3
ELMOD3
Q96FG2 ELMO domain containing 3 Signaling 11 0.821 0.269 5.0E-16 0.010 None 1.000 1 0 2019 2019
Entrez Id: 2706
Gene Symbol: GJB2
GJB2
P29033 gap junction protein beta 2 Cell-cell junction 392 0.441 0.846 6.6E-16 0.400 definitive 1.000 25 1 1997 2019
Entrez Id: 161497
Gene Symbol: STRC
STRC
Q7RTU9 stereocilin Extracellular structure 25 0.700 0.192 1.8E-15 0.010 None 1.000 1 0 2009 2009
Entrez Id: 81624
Gene Symbol: DIAPH3
DIAPH3
Q9NSV4 diaphanous related formin 3 44 0.656 0.462 2.0E-15 0.010 None 1.000 1 0 2016 2016
Entrez Id: 822
Gene Symbol: CAPG
CAPG
P40121 capping actin protein, gelsolin like Cellular structure 111 0.548 0.731 9.4E-14 0.010 None 1.000 1 0 2019 2019
Entrez Id: 1811
Gene Symbol: SLC26A3
SLC26A3
P40879 solute carrier family 26 member 3 Transporter 128 0.554 0.692 1.4E-13 0.010 None 1.000 1 0 2017 2017
Entrez Id: 51761
Gene Symbol: ATP8A2
ATP8A2
Q9NTI2 ATPase phospholipid transporting 8A2 Transporter 55 0.659 0.577 1.2E-12 0.010 None 1.000 1 0 2014 2014
Entrez Id: 64699
Gene Symbol: TMPRSS3
TMPRSS3
P57727 transmembrane serine protease 3 Enzyme 45 0.650 0.538 6.1E-11 0.060 None 1.000 6 0 1997 2018
Entrez Id: 146183
Gene Symbol: OTOA
OTOA
Q7RTW8 otoancorin Extracellular structure 12 0.760 0.423 3.0E-10 0.010 None 1.000 1 0 2002 2002
Entrez Id: 79955
Gene Symbol: PDZD7
PDZD7
Q9H5P4 PDZ domain containing 7 45 0.659 0.385 7.6E-10 0.310 definitive 1.000 10 0 2009 2018
Entrez Id: 525
Gene Symbol: ATP6V1B1
ATP6V1B1
P15313 ATPase H+ transporting V1 subunit B1 Transporter 30 0.695 0.346 2.4E-09 0.200 None 1.000 1 0 2017 2017
Entrez Id: 83715
Gene Symbol: ESPN
ESPN
B1AK53 espin Cellular structure 28 0.700 0.385 2.9E-09 0.010 None 1.000 1 0 2004 2004
Entrez Id: 6583
Gene Symbol: SLC22A4
SLC22A4
Q9H015 solute carrier family 22 member 4 Transporter 90 0.603 0.769 1.8E-08 0.010 None 1.000 1 0 2013 2013
Entrez Id: 494513
Gene Symbol: PJVK
PJVK
Q0ZLH3 pejvakin 15 0.769 0.115 3.7E-08 0.010 None 1.000 1 0 2016 2016
Entrez Id: 10804
Gene Symbol: GJB6
GJB6
O95452 gap junction protein beta 6 Cell-cell junction 176 0.528 0.808 1.7E-07 0.040 None 1.000 4 0 2004 2014
Entrez Id: 53405
Gene Symbol: CLIC5
CLIC5
Q9NZA1 chloride intracellular channel 5 Ion channel 11 0.792 0.308 1.6E-06 0.300 moderate 1.000 3 0 2006 2015
Entrez Id: 64072
Gene Symbol: CDH23
CDH23
Q9H251 cadherin related 23 203 0.539 0.769 3.2E-06 0.320 moderate 1.000 2 0 2001 2019
Entrez Id: 124842
Gene Symbol: TMEM132E
TMEM132E
Q6IEE7 transmembrane protein 132E 7 0.805 0.231 4.5E-05 0.300 limited 1.000 1 0 2015 2015
Entrez Id: 25861
Gene Symbol: WHRN
WHRN
Q9P202 whirlin Cellular structure 50 0.670 0.385 7.7E-05 0.010 None 1.000 1 0 2003 2003
Entrez Id: 23562
Gene Symbol: CLDN14
CLDN14
O95500 claudin 14 Cell-cell junction 36 0.705 0.462 1.1E-04 0.010 None 1.000 1 0 2001 2001