Entrez Id: |
4508 |
Gene Symbol: |
ATP6 |
ATP6
|
P00846
|
ATP synthase F0 subunit 6
|
Transporter
|
226
|
0.541 |
0.731 |
|
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
80208 |
Gene Symbol: |
SPG11 |
SPG11
|
Q96JI7
|
SPG11 vesicle trafficking associated, spatacsin
|
|
139
|
0.576 |
0.538 |
1.6E-39 |
0.100 |
None
|
1.000 |
1
|
2
|
2009 |
2009 |
Entrez Id: |
8291 |
Gene Symbol: |
DYSF |
DYSF
|
O75923
|
dysferlin
|
Transporter
|
144
|
0.582 |
0.692 |
3.7E-33 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
10585 |
Gene Symbol: |
POMT1 |
POMT1
|
Q9Y6A1
|
protein O-mannosyltransferase 1
|
|
223
|
0.525 |
0.615 |
4.2E-17 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
2581 |
Gene Symbol: |
GALC |
GALC
|
P54803
|
galactosylceramidase
|
|
99
|
0.604 |
0.615 |
5.2E-15 |
0.100 |
None
|
|
0
|
2
|
|
|
Entrez Id: |
5339 |
Gene Symbol: |
PLEC |
PLEC
|
Q15149
|
plectin
|
Cellular structure
|
218
|
0.523 |
0.808 |
8.3E-12 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
29954 |
Gene Symbol: |
POMT2 |
POMT2
|
Q9UKY4
|
protein O-mannosyltransferase 2
|
|
177
|
0.544 |
0.615 |
9.4E-12 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
1384 |
Gene Symbol: |
CRAT |
CRAT
|
P43155
|
carnitine O-acetyltransferase
|
Enzyme
|
59
|
0.656 |
0.577 |
9.5E-12 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
6389 |
Gene Symbol: |
SDHA |
SDHA
|
P31040
|
succinate dehydrogenase complex flavoprotein subunit A
|
Enzyme
|
246
|
0.517 |
0.731 |
2.6E-10 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
29925 |
Gene Symbol: |
GMPPB |
GMPPB
|
Q9Y5P6
|
GDP-mannose pyrophosphorylase B
|
|
158
|
0.578 |
0.538 |
8.4E-07 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
11154 |
Gene Symbol: |
AP4S1 |
AP4S1
|
Q9Y587
|
adaptor related protein complex 4 subunit sigma 1
|
Transporter
|
64
|
0.674 |
0.385 |
1.7E-06 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
11149 |
Gene Symbol: |
BVES |
BVES
|
Q8NE79
|
blood vessel epicardial substance
|
|
43
|
0.722 |
0.308 |
9.3E-06 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
79147 |
Gene Symbol: |
FKRP |
FKRP
|
Q9H9S5
|
fukutin related protein
|
|
248
|
0.513 |
0.731 |
9.8E-06 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
6390 |
Gene Symbol: |
SDHB |
SDHB
|
P21912
|
succinate dehydrogenase complex iron sulfur subunit B
|
Enzyme
|
316
|
0.474 |
0.846 |
2.4E-04 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
154881 |
Gene Symbol: |
KCTD7 |
KCTD7
|
Q96MP8
|
potassium channel tetramerization domain containing 7
|
Enzyme modulator
|
68
|
0.650 |
0.423 |
6.3E-04 |
0.100 |
None
|
|
0
|
2
|
|
|
Entrez Id: |
50484 |
Gene Symbol: |
RRM2B |
RRM2B
|
Q7LG56
|
ribonucleotide reductase regulatory TP53 inducible subunit M2B
|
Enzyme
|
238
|
0.527 |
0.769 |
2.4E-03 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
56652 |
Gene Symbol: |
TWNK |
TWNK
|
Q96RR1
|
twinkle mtDNA helicase
|
Enzyme
|
245
|
0.516 |
0.692 |
3.2E-03 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
4137 |
Gene Symbol: |
MAPT |
MAPT
|
P10636
|
microtubule associated protein tau
|
|
469
|
0.446 |
0.923 |
6.0E-03 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
1674 |
Gene Symbol: |
DES |
DES
|
P17661
|
desmin
|
|
330
|
0.460 |
0.846 |
8.8E-03 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
246243 |
Gene Symbol: |
RNASEH1 |
RNASEH1
|
O60930
|
ribonuclease H1
|
|
52
|
0.711 |
0.462 |
1.1E-02 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
103 |
Gene Symbol: |
ADAR |
ADAR
|
P55265
|
adenosine deaminase RNA specific
|
Enzyme
|
256
|
0.501 |
0.808 |
2.6E-02 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
644096 |
Gene Symbol: |
SDHAF1 |
SDHAF1
|
A6NFY7
|
succinate dehydrogenase complex assembly factor 1
|
|
88
|
0.656 |
0.462 |
8.7E-02 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
84668 |
Gene Symbol: |
FAM126A |
FAM126A
|
Q9BYI3
|
family with sequence similarity 126 member A
|
|
50
|
0.682 |
0.423 |
0.12 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
79152 |
Gene Symbol: |
FA2H |
FA2H
|
Q7L5A8
|
fatty acid 2-hydroxylase
|
Enzyme
|
131
|
0.573 |
0.654 |
0.15 |
0.100 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
55697 |
Gene Symbol: |
VAC14 |
VAC14
|
Q08AM6
|
VAC14 component of PIKFYVE complex
|
Receptor
|
140
|
0.588 |
0.731 |
0.19 |
0.100 |
None
|
|
0
|
0
|
|
|