Gene Uniprot Gene Full Name Protein Class pLI DSI v DPI v
FXN Q16595 frataxin Enzyme 0.34 0.510 0.654
OPA3 Q9H6K4 outer mitochondrial membrane lipid metabolism regulator OPA3 0.57 0.653 0.385
SPG7 Q9UQ90 SPG7 matrix AAA peptidase subunit, paraplegin Enzyme 2.0E-36 0.436 0.885
TAZ Q16635 tafazzin Enzyme 0.73 0.477 0.808