Gene Uniprot Gene Full Name Protein Class pLI DSI v DPI v
ABCC8 Q09428 ATP binding cassette subfamily C member 8 Transporter 8.0E-24 0.474 0.846
ACADM P11310 acyl-CoA dehydrogenase medium chain Enzyme 2.1E-12 0.638 0.462
ALDOB P05062 aldolase, fructose-bisphosphate B 7.9E-07 0.623 0.538
ASL P04424 argininosuccinate lyase Enzyme 8.6E-10 0.593 0.731
ASPA P45381 aspartoacylase 4.1E-04 0.564 0.731
ASS1 P00966 argininosuccinate synthase 1 Enzyme 1.5E-09 0.523 0.731
BCKDHA P12694 branched chain keto acid dehydrogenase E1 subunit alpha 9.8E-09 0.695 0.423
BCKDHB P21953 branched chain keto acid dehydrogenase E1 subunit beta Enzyme 4.3E-09 0.682 0.500
BTD P43251 biotinidase Enzyme 1.5E-07 0.628 0.654
CACNA1A O00555 calcium voltage-gated channel subunit alpha1 A Ion channel 1.00 0.489 0.769
CPS1 P31327 carbamoyl-phosphate synthase 1 Enzyme 1.1E-09 0.590 0.615
CPT1A P50416 carnitine palmitoyltransferase 1A Enzyme 5.1E-09 0.555 0.808
CPT2 P23786 carnitine palmitoyltransferase 2 Enzyme 4.6E-10 0.542 0.769
DBT P11182 dihydrolipoamide branched chain transacylase E2 Enzyme 1.0E-05 0.638 0.462
FBP1 P09467 fructose-bisphosphatase 1 Enzyme 7.9E-02 0.575 0.692
GK P32189 glycerol kinase Kinase 0.99 0.656 0.577
HADHA P40939 hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha Enzyme 4.4E-06 0.569 0.769
HADHB P55084 hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta Enzyme 1.5E-11 0.619 0.692
HLCS P50747 holocarboxylase synthetase Enzyme 1.9E-08 0.650 0.654
HMGCL P35914 3-hydroxy-3-methylglutaryl-CoA lyase Enzyme 2.6E-06 0.691 0.462
HNF1A P20823 HNF1 homeobox A Nucleic acid binding 0.96 0.478 0.846
HNF4A P41235 hepatocyte nuclear factor 4 alpha Nuclear receptor 0.15 0.461 0.808
IVD P26440 isovaleryl-CoA dehydrogenase Enzyme 1.5E-14 0.705 0.462
KCNJ11 Q14654 potassium inwardly rectifying channel subfamily J member 11 Ion channel 1.1E-02 0.529 0.615
MCCC1 Q96RQ3 methylcrotonoyl-CoA carboxylase 1 Enzyme 4.0E-12 0.700 0.308