Gene Uniprot Gene Full Name Protein Class pLI DSI v DPI v
POLG P54098 DNA polymerase gamma, catalytic subunit Enzyme 2.1E-09 0.457 0.846
DHCR7 Q9UBM7 7-dehydrocholesterol reductase Enzyme 3.9E-13 0.500 0.846
TAZ Q16635 tafazzin Enzyme 0.73 0.477 0.808
ACAD8 Q9UKU7 acyl-CoA dehydrogenase family member 8 Enzyme 5.6E-14 0.506 0.885
HTRA2 O43464 HtrA serine peptidase 2 3.6E-03 0.542 0.692
ECHS1 P30084 enoyl-CoA hydratase, short chain 1 Enzyme 8.8E-04 0.601 0.654
TMEM70 Q9BUB7 transmembrane protein 70 2.9E-02 0.636 0.654
ATAD3A Q9NVI7 ATPase family AAA domain containing 3A Enzyme 4.1E-09 0.628 0.692
OPA3 Q9H6K4 outer mitochondrial membrane lipid metabolism regulator OPA3 0.57 0.653 0.385
CLPB Q9H078 caseinolytic mitochondrial matrix peptidase chaperone subunit B 5.0E-04 0.631 0.654
ATP5F1D P30049 ATP synthase F1 subunit delta Transporter 7.4E-02 0.674 0.500
AGK Q53H12 acylglycerol kinase 6.0E-09 0.650 0.654
SERAC1 Q96JX3 serine active site containing 1 3.9E-06 0.686 0.385
DNAJC19 Q96DA6 DnaJ heat shock protein family (Hsp40) member C19 6.1E-04 0.663 0.577
TIMM50 Q3ZCQ8 translocase of inner mitochondrial membrane 50 1.8E-03 0.678 0.500
AUH Q13825 AU RNA binding methylglutaconyl-CoA hydratase Enzyme 8.0E-06 0.686 0.346
ATP5F1E P56381 ATP synthase F1 subunit epsilon Transporter 8.9E-03 0.686 0.500
MICOS13 Q5XKP0 mitochondrial contact site and cristae organizing system subunit 13 8.3E-04 0.736 0.346
ACADSB P45954 acyl-CoA dehydrogenase short/branched chain 2.7E-11 0.691 0.500
ATPAF2 Q8N5M1 ATP synthase mitochondrial F1 complex assembly factor 2 2.2E-09 0.729 0.423