Gene Uniprot Gene Full Name Protein Class pLI DSI v DPI v
SQSTM1 Q13501 sequestosome 1 8.6E-04 0.428 0.885
SPG7 Q9UQ90 SPG7 matrix AAA peptidase subunit, paraplegin Enzyme 2.0E-36 0.436 0.885
VCP P55072 valosin containing protein 1.00 0.469 0.923
IFIH1 Q9BYX4 interferon induced with helicase C domain 1 7.0E-44 0.471 0.808
FUS P35637 FUS RNA binding protein Nucleic acid binding 1.00 0.470 0.846
C9orf72 Q96LT7 C9orf72-SMCR8 complex subunit 1.1E-06 0.496 0.769
TARDBP Q13148 TAR DNA binding protein 0.99 0.493 0.808
POLR3A O14802 RNA polymerase III subunit A Enzyme 1.3E-23 0.538 0.769
TBK1 Q9UHD2 TANK binding kinase 1 Kinase 7.5E-02 0.513 0.846
ALDH18A1 P54886 aldehyde dehydrogenase 18 family member A1 Enzyme 8.1E-04 0.551 0.769
SIGMAR1 Q99720 sigma non-opioid intracellular receptor 1 0.17 0.544 0.808
SPG11 Q96JI7 SPG11 vesicle trafficking associated, spatacsin 1.6E-39 0.576 0.538
TYROBP O43914 transmembrane immune signaling adaptor TYROBP 0.20 0.573 0.769
SETX Q7Z333 senataxin Enzyme 0.95 0.570 0.731
CHCHD10 Q8WYQ3 coiled-coil-helix-coiled-coil-helix domain containing 10 5.4E-06 0.623 0.462
GBE1 Q04446 1,4-alpha-glucan branching enzyme 1 Enzyme 1.1E-12 0.612 0.654
MATR3 P43243 matrin 3 1.00 0.631 0.538
ERLIN2 O94905 ER lipid raft associated 2 6.7E-04 0.647 0.500
ALS2 Q96Q42 alsin Rho guanine nucleotide exchange factor ALS2 8.7E-12 0.647 0.423
POLR3B Q9NW08 RNA polymerase III subunit B Enzyme 1.7E-23 0.628 0.654