Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
BEFREE |
Cystic Fibrosis of the Pancreas: The Role of CFTR Channel in the Regulation of Intracellular Ca<sup>2+</sup> Signaling and Mitochondrial Function in the Exocrine Pancreas.
|
30618777 |
2018 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
BEFREE |
CFTR gene transfer to human cystic fibrosis pancreatic duct cells using a Sendai virus vector.
|
17654517 |
2008 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
BEFREE |
Expression of a wild-type CFTR maintains the integrity of the biosynthetic/secretory pathway in human cystic fibrosis pancreatic duct cells.
|
15956032 |
2005 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Restoration of W1282X CFTR activity by enhanced expression.
|
17541014 |
2007 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
A mouse model for the delta F508 allele of cystic fibrosis.
|
7560099 |
1995 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation.
|
21083385 |
2010 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Development of novel aminoglycoside (NB54) with reduced toxicity and enhanced suppression of disease-causing premature stop mutations.
|
19309154 |
2009 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Proteasome-dependent pharmacological rescue of cystic fibrosis transmembrane conductance regulator revealed by mutation of glycine 622.
|
18230692 |
2008 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Functional insertion of the SV40 large T oncogene in cystic fibrosis intestinal epithelium. Characterization of CFI-3 cells.
|
1718974 |
1991 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
The TNFalpha receptor TNFRSF1A and genes encoding the amiloride-sensitive sodium channel ENaC as modulators in cystic fibrosis.
|
16463024 |
2006 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
|
17347447 |
2007 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Correction of CFTR malfunction and stimulation of Ca-activated Cl channels restore HCO3- secretion in cystic fibrosis bile ductular cells.
|
11786964 |
2002 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770.
|
19846789 |
2009 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Cystic fibrosis in 65- and 67-year-old siblings. Clinical feature and nasal potential difference measurement in patients with genotypes F508del and 2789+5G-->A.
|
16763370 |
2006 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Evidence that systemic gentamicin suppresses premature stop mutations in patients with cystic fibrosis.
|
11401894 |
2001 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Nonsense-mediated mRNA decay affects nonsense transcript levels and governs response of cystic fibrosis patients to gentamicin.
|
17290305 |
2007 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Cystic fibrosis transmembrane regulator potentiators as promising cystic fibrosis therapies.
|
21303308 |
2011 |
Fibrocystic Disease of Pancreas
|
0.330 |
Biomarker
|
disease |
CTD_human |
Probing conformational rescue induced by a chemical corrector of F508del-cystic fibrosis transmembrane conductance regulator (CFTR) mutant.
|
21602569 |
2011 |