HMGCL |
P35914
|
3-hydroxy-3-methylglutaryl-CoA lyase
|
Enzyme
|
2.6E-06 |
0.691 |
0.462 |
ACADM |
P11310
|
acyl-CoA dehydrogenase medium chain
|
Enzyme
|
2.1E-12 |
0.638 |
0.462 |
ALDOB |
P05062
|
aldolase, fructose-bisphosphate B
|
|
7.9E-07 |
0.623 |
0.538 |
ASL |
P04424
|
argininosuccinate lyase
|
Enzyme
|
8.6E-10 |
0.593 |
0.731 |
ASS1 |
P00966
|
argininosuccinate synthase 1
|
Enzyme
|
1.5E-09 |
0.523 |
0.731 |
ASPA |
P45381
|
aspartoacylase
|
|
4.1E-04 |
0.564 |
0.731 |
ABCC8 |
Q09428
|
ATP binding cassette subfamily C member 8
|
Transporter
|
8.0E-24 |
0.474 |
0.846 |
BTD |
P43251
|
biotinidase
|
Enzyme
|
1.5E-07 |
0.628 |
0.654 |
BCKDHA |
P12694
|
branched chain keto acid dehydrogenase E1 subunit alpha
|
|
9.8E-09 |
0.695 |
0.423 |
BCKDHB |
P21953
|
branched chain keto acid dehydrogenase E1 subunit beta
|
Enzyme
|
4.3E-09 |
0.682 |
0.500 |
CACNA1A |
O00555
|
calcium voltage-gated channel subunit alpha1 A
|
Ion channel
|
1.00 |
0.489 |
0.769 |
CPS1 |
P31327
|
carbamoyl-phosphate synthase 1
|
Enzyme
|
1.1E-09 |
0.590 |
0.615 |
CPT1A |
P50416
|
carnitine palmitoyltransferase 1A
|
Enzyme
|
5.1E-09 |
0.555 |
0.808 |
CPT2 |
P23786
|
carnitine palmitoyltransferase 2
|
Enzyme
|
4.6E-10 |
0.542 |
0.769 |
DBT |
P11182
|
dihydrolipoamide branched chain transacylase E2
|
Enzyme
|
1.0E-05 |
0.638 |
0.462 |
POLG |
P54098
|
DNA polymerase gamma, catalytic subunit
|
Enzyme
|
2.1E-09 |
0.457 |
0.846 |
FBP1 |
P09467
|
fructose-bisphosphatase 1
|
Enzyme
|
7.9E-02 |
0.575 |
0.692 |
GK |
P32189
|
glycerol kinase
|
Kinase
|
0.99 |
0.656 |
0.577 |
HNF4A |
P41235
|
hepatocyte nuclear factor 4 alpha
|
Nuclear receptor
|
0.15 |
0.461 |
0.808 |
HNF1A |
P20823
|
HNF1 homeobox A
|
Nucleic acid binding
|
0.96 |
0.478 |
0.846 |
HLCS |
P50747
|
holocarboxylase synthetase
|
Enzyme
|
1.9E-08 |
0.650 |
0.654 |
HADHA |
P40939
|
hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
|
Enzyme
|
4.4E-06 |
0.569 |
0.769 |
HADHB |
P55084
|
hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
|
Enzyme
|
1.5E-11 |
0.619 |
0.692 |
IVD |
P26440
|
isovaleryl-CoA dehydrogenase
|
Enzyme
|
1.5E-14 |
0.705 |
0.462 |
MEN1 |
O00255
|
menin 1
|
|
1.00 |
0.444 |
0.808 |