MCCC1 |
Q96RQ3
|
methylcrotonoyl-CoA carboxylase 1
|
Enzyme
|
4.0E-12 |
0.700 |
0.308 |
SLC25A15 |
Q9Y619
|
solute carrier family 25 member 15
|
Transporter
|
3.7E-07 |
0.711 |
0.346 |
MMAA |
Q8IVH4
|
metabolism of cobalamin associated A
|
|
9.4E-13 |
0.743 |
0.346 |
BCKDHA |
P12694
|
branched chain keto acid dehydrogenase E1 subunit alpha
|
|
9.8E-09 |
0.695 |
0.423 |
MCCC2 |
Q9HCC0
|
methylcrotonoyl-CoA carboxylase 2
|
Enzyme
|
4.5E-11 |
0.674 |
0.423 |
NAGS |
Q8N159
|
N-acetylglutamate synthase
|
|
4.0E-08 |
0.716 |
0.423 |
ACADM |
P11310
|
acyl-CoA dehydrogenase medium chain
|
Enzyme
|
2.1E-12 |
0.638 |
0.462 |
DBT |
P11182
|
dihydrolipoamide branched chain transacylase E2
|
Enzyme
|
1.0E-05 |
0.638 |
0.462 |
HMGCL |
P35914
|
3-hydroxy-3-methylglutaryl-CoA lyase
|
Enzyme
|
2.6E-06 |
0.691 |
0.462 |
IVD |
P26440
|
isovaleryl-CoA dehydrogenase
|
Enzyme
|
1.5E-14 |
0.705 |
0.462 |
BCKDHB |
P21953
|
branched chain keto acid dehydrogenase E1 subunit beta
|
Enzyme
|
4.3E-09 |
0.682 |
0.500 |
SLC25A13 |
Q9UJS0
|
solute carrier family 25 member 13
|
Transporter
|
1.3E-24 |
0.617 |
0.500 |
ALDOB |
P05062
|
aldolase, fructose-bisphosphate B
|
|
7.9E-07 |
0.623 |
0.538 |
PCCA |
P05165
|
propionyl-CoA carboxylase subunit alpha
|
Enzyme
|
3.1E-15 |
0.682 |
0.538 |
MMAB |
Q96EY8
|
metabolism of cobalamin associated B
|
Enzyme
|
4.1E-03 |
0.695 |
0.538 |
GK |
P32189
|
glycerol kinase
|
Kinase
|
0.99 |
0.656 |
0.577 |
PCCB |
P05166
|
propionyl-CoA carboxylase subunit beta
|
Enzyme
|
1.5E-08 |
0.695 |
0.577 |
CPS1 |
P31327
|
carbamoyl-phosphate synthase 1
|
Enzyme
|
1.1E-09 |
0.590 |
0.615 |
KCNJ11 |
Q14654
|
potassium inwardly rectifying channel subfamily J member 11
|
Ion channel
|
1.1E-02 |
0.529 |
0.615 |
BTD |
P43251
|
biotinidase
|
Enzyme
|
1.5E-07 |
0.628 |
0.654 |
HLCS |
P50747
|
holocarboxylase synthetase
|
Enzyme
|
1.9E-08 |
0.650 |
0.654 |
SLC7A7 |
Q9UM01
|
solute carrier family 7 member 7
|
Transporter
|
8.0E-07 |
0.603 |
0.654 |
FBP1 |
P09467
|
fructose-bisphosphatase 1
|
Enzyme
|
7.9E-02 |
0.575 |
0.692 |
HADHB |
P55084
|
hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
|
Enzyme
|
1.5E-11 |
0.619 |
0.692 |
ASL |
P04424
|
argininosuccinate lyase
|
Enzyme
|
8.6E-10 |
0.593 |
0.731 |